No abstract available
MeSH terms
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Carrier Proteins / metabolism
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Cystic Fibrosis / genetics
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Cystic Fibrosis Transmembrane Conductance Regulator / metabolism
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Endoplasmic Reticulum / chemistry
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Endoplasmic Reticulum / metabolism*
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Endoplasmic Reticulum Chaperone BiP
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Genetic Predisposition to Disease / genetics*
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HSP70 Heat-Shock Proteins / metabolism
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Heat-Shock Proteins*
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Humans
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Lysosomal Storage Diseases / genetics
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Membrane Proteins / metabolism
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Molecular Chaperones / genetics
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Molecular Chaperones / metabolism
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Molecular Chaperones / physiology*
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Mutation
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Protein Folding*
Substances
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CFTR protein, human
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Carrier Proteins
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Endoplasmic Reticulum Chaperone BiP
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HSP70 Heat-Shock Proteins
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Heat-Shock Proteins
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Membrane Proteins
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Molecular Chaperones
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glucose-regulated proteins
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Cystic Fibrosis Transmembrane Conductance Regulator